To investigate the clinical and pathological features of eosinophilic fasciitis (EF). Methods: The clinical presentation, laboratory examination, imaging characteristics, and pathological features of two patients diagnosed with EF were retrospectively analyzed, and the literature was reviewed. Results: The 2 cases (1 female and 1 male) presented with symmetrical edema and stiffening of the limbs. Peripheral eosinophilic granulocyte increase and increased erythrocyte sedimentation rate were present in both cases, and hypergammaglobulinemia and increased C-reactive protein were found in 1 case. Muscle MRI revealed thickening and high signal intensity on T2WI in deep fasciae. Full-thickness wedge biopsy of the clinically affected skin and muscle showed thickening of the muscular fascia with accumulation of inflammatory cells. We reviewed the reported data of 496 cases of EF. Most of the patients presented with symmetrical edema and stiffening of the limbs. The characteristic laboratory findings in EF were peripheral eosinophilia, increased erythrocyte sedimentation rate, and hypergammaglobulinemia. Muscle MRI characteristics of EF were thickening on T1-weighted images, increased signal intensity on T2-weighted images, and contrast enhancement in thickened muscle fascia following gadolinium injection. Pathological features of EF were fascial thickening and fibrosis and inflammatory cell infiltration. Conclusion: EF is a rare disorder characterized by symmetrical edema and stiffening of the limbs, peripheral eosinophilia, hypergammaglobulinemia, and increased erythrocyte sedimentation rate. Systemic involvement is rare, and corticosteroid treatment is effective．